By Sinéad L. Murphy; Kennith Fang, MD; Tabitha Moe, MD
Abstract
A persistent Left Superior Vena Cava (LSVC) is a relatively common, quiescent congenital anomaly in the general population, often with drainage into the coronary sinus and return to the right atrium. We present a rare case of persistent LSVC with connection to the Left Upper Pulmonary Vein (LUPV), creating potential for right-to-left shunting, in the absence of other congenital anatomical anomalies. This connection can result in cyanosis, increased risk for endocarditis and, as seen in this patient, paradoxical thromboembolism. A discussion of morphologic forms, diagnostic imaging, clinical significance, and potential corrective procedures is reviewed.
To read the full article, please go to the August 2017 Issue of CCT, where it was originally published.